CASE REPORT
Year : 2014  |  Volume : 7  |  Issue : 6  |  Page : 773-776

Intraoral hemangiomas in Sturge-Weber syndrome


1 Department of Anaesthesiology, Dr. D. Y. Patil Medical College, Hospital and Research Centre, Navi Mumbai, Maharashtra, India
2 Department of Anaesthesiology, Dr. D. Y. Patil Medical College, Hospital and Research Centre, Dr. D. Y. Patil Vidyapeeth, Pune, Maharashtra, India

Correspondence Address:
Sonal S Khatavkar
Flat S2, Bldg B1, Tejovalya, Raviraj CHSL, Near Cipla Foundation, Warje, Pune - 411 058, Maharashtra
India
Login to access the Email id

Source of Support: None, Conflict of Interest: None


DOI: 10.4103/0975-2870.144879

Rights and Permissions

Sturge-Weber syndrome is a rare congenital disease also called as encephalo-trigeminal-angiomatosis, caused by persistence of transitory primordial arterio-venous connections of fetal intracranial vasculature. It is characterized by vascular malformations with capillary venous angiomas that involve face, choroid of eye, and leptomeninges. The main clinical features of this syndrome are port-wine stains, glaucoma, convulsions and angiomas of the airway. Anesthesia management is directed towards keeping the intracranial and intraocular pressures normal, avoiding trauma to hemangiomas, and anticipating difficult airway. We discuss the case of a 13-year-old boy with intraoral hemangiomas resulting in difficulty in speech. Patient was scheduled for digital subtraction angiography (DSA) and sclerotherapy of hemangiomas under general anesthesia. The anesthetic considerations during the peri-operative management, including airway problems, multiple changes in patient position during DSA procedure, precautions during use of radio-contrast media and sclerosing agents are highlighted.


[FULL TEXT] [PDF]*
Print this article     Email this article
 Next article
 Previous article
 Table of Contents

 Similar in PUBMED
   Search Pubmed for
   Search in Google Scholar for
 Related articles
 Citation Manager
 Access Statistics
 Reader Comments
 Email Alert *
 Add to My List *
 * Requires registration (Free)
 

 Article Access Statistics
    Viewed2638    
    Printed125    
    Emailed0    
    PDF Downloaded215    
    Comments [Add]    

Recommend this journal