CASE REPORT
Year : 2014  |  Volume : 7  |  Issue : 6  |  Page : 790-792

Atypical Nonne-Milroy syndrome: Complicated with chylous effusion


1 Department of Pulmonary Medicine, Burdwan Medical College, Burdwan, India
2 Calcutta National Medical College, Kolkata, West Bengal, India

Correspondence Address:
Kaushik Saha
Department of Pulmonary Medicine, Burdwan Medical College, Burdwan, Rabindra Pally, 1st Lane, P. O - Nimta, Kolkata - 700 049, West Bengal
India
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Source of Support: None, Conflict of Interest: None


DOI: 10.4103/0975-2870.144886

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Nonne-Milroy syndrome is a rare primary lymphedema characterized by firm non-pitting edema of the lower extremities of the whole leg or may be limited to the feet or toes since birth or infancy. We are reporting a 51-year-old male who presented with dry cough for the previous 7 months and dyspnea for the previous 4 months due to bilateral chylous effusion and that was associated with firm edema of the lower extremities, was waxing and waning since birth. Duplex ultrasound of the lower limbs showed patent blood vessels. Lymphoscintigraphy demonstrated aplasia of the lymphatics in both lower limbs. The patient was diagnosed as primary lymphedema or Nonne-Milroy syndrome after excluding other congenital causes of primary edema. He was treated by bilateral pleurodesis with tetracycline for his chylous effusion and no recurrence was observed after 1 year of follow-up.


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