Year : 2015  |  Volume : 8  |  Issue : 6  |  Page : 781-784

Isolated right pulmonary artery agenesis with aplasia of right upper lobe and with anomalous arterial supply from celiac axis, anomalous venous drainage

1 Department of Radiodiagnosis, D.Y. Patil Medical College and Hospital, Pune, Maharashtra, India
2 Department of Radiodiagnosis, Radiolofy Resident, KEM Hospital, Pune, Maharashtra, India

Correspondence Address:
Tushar Madhav Kalekar
Department of Radiodiagnosis, D.Y. Patil Medical College and Hospital, Pune, Maharashtra
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Source of Support: None, Conflict of Interest: None

DOI: 10.4103/0975-2870.169930

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Pulmonary artery agenesis is the complete absence of the right or left pulmonary artery. This lesion is commonly associated with other cardiac anomalies and is usually diagnosed incidentally. Unilateral absence of pulmonary artery with lung hypoplasia is very rare. Ipsilateral hypoplastic or absent central pulmonary artery in these patients will have a systemic arterial supply to peripheral pulmonary arteries of the affected lung from the descending thoracic or upper abdominal aorta. These findings are usually characterized as pulmonary veno lobar syndrome or scimitar syndrome when associated with ipsilateral total or partial anomalous pulmonary venous return from the lower lobe which drains into the inferior vena cava or less commonly to the hepatic, azygous, or portal vein, or into the right atrium and lung agenesis/hypoplasia.

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